J Med Life Sci > Volume 11(2); 2014 > Article
Journal of Medicine and Life Science 2014;11(2):115-117.
DOI: https://doi.org/10.22730/jmls.2014.11.2.115    Published online December 18, 2018.
선천성 난청을 동반한 일측성 와우신경 부전증 1예
, , ,
A case of unilateral cochlear nerve deficiency with congenital hearing loss
Han-Bin Jang, Dong Young Kim, Chan Il Song, Se-Hyung Kim
The narrow bony cochlear nerve canal in high resolution temporal bone computed tomography (TBCT) is frequently found in patients of congenital sensorineural hearing loss. But this bony structural anomaly could not conclude the functional outcome of cochlear nerve. Here we present a case of a 10-month-old girl having unilateral narrow bony cochlear nerve canals. In internal auditory magnetic resonance imaging (IAC MRI), the right cochlear nerve was not identified to be intact. Moreover, acoustic brainstem response threshold and automated acoustic brainstem response revealed nearly deaf hearing threshold. Therefore we suggest that congenital hearing loss patients take TBCT and IAC MRI to rule out the narrow bony cochlear nerve canal.
Key Words: cochlear nerve deficiency; magnetic resonance imaging; sensorineural hearing loss; unilateral hearing loss
METRICS Graph View
  • 0 Crossref
  •  0 Scopus
  • 449 View
  • 3 Download
Related articles

Editorial Office
102, Jejudaehak-ro, Jeju-si, Jeju-do 63243, Republic of Korea
Tel: +82-64-754-8023    E-mail: jmls.jeju@gmail.com                

Copyright © 2023 by Jeju National University Institute for Medical Science.

Developed in M2PI

Close layer
prev next