J Med Life Sci > Volume 9(2); 2012 > Article
Journal of Medicine and Life Science 2012;9(2):110-113.
DOI: https://doi.org/10.22730/jmls.2012.9.2.110    Published online December 18, 2012.
A case of juvenile dermatomyositis with esophago-pleural fistula caused by spontaneous lower esophageal perforation
Kyung-Sue Shin
Department of Pediatrics, Jeju National University School of Medicine, Jeju, Korea
Correspondence:  Kyung-Sue Shin, Email: kyungsue@jejunu.ac.kr
Received: 28 November 2012   • Revised: 5 December 2012   • Accepted: 12 December 2012
Juvenile dermatomyositis (JDM) is a multisystem disease of uncertain origin that results in nonsuppurative inflammation of striated muscle and skin. Gastrointestinal perforation including esophagus is a well-recognized complication of JDM. A one year and nine months old girl with JDM was recently seen with esophago-pleural fistula. The fistula was caused by spontaneous lower esophageal perforation near the gastro-esophageal junction. The treatment consisted of adequate drainage of perforation site, total parenteral nutrition, long-term intravenous hydrocortisone, and broad-spectrum antibiotics. Although the duration of the fistula closing was long, the fistula spontaneously obliterated without other surgical management. This is a rare case of JDM with esophago-pleural fistula caused by spontaneous lower esophageal perforation.
Key Words: Juvenile dermatomyositis; fistula; esophageal perforation

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